Abstract
Background and Study Aims Tufted angiomas (TAs) are rare, benign vascular neoplasms of childhood mainly localized
in the skin and subcutaneous tissues. TAs are progressive, slowly growing, and characteristically
involve superficial or deep muscle fascia tissue. TAs are frequently seen before the
age of 5 years (60 to 70%) and have no sex predominance. TA following pregnancy or
TA among immunosuppressive drug users was rarely reported in literature. TA is extremely
rare in patients older than 60 years.
Patient A 73-year-old man presented with right eye pain, redness, burning sensation, swelling,
and double vision. On physical examination, his right eye was protruding, hyperemic,
and there was a supraorbital palpable mass extending to the lateral orbital wall.
Cranial computed tomography and magnetic resonance imaging revealed a heterogeneously
enhancing right intraorbital retrobulbar capsulated lesion with intracranial extension.
The patient underwent surgery. TA was proven histopathologically.
Conclusion We report the first TA of the orbit with orbital and cranial bone destruction, frontotemporal
extension, and loss of vision due to optic nerve compression. The surgical treatment
and orbitocranial mesh reconstruction following neurosurgical gross total removal
of the lesion is discussed. TAs should be considered in the differential diagnosis
of intraorbital tumors. TAs usually persist throughout life but cause no serious symptoms
when they are located in the upper thorax, neck, and shoulders. TAs located in the
orbit should be excised.
Keywords
tufted angioma - orbit - reconstruction - titanium mash
